產(chǎn)品詳情
簡單介紹：
Anti-BPGM抗體產(chǎn)品質量穩(wěn)定，實驗效果明顯，貨期快，價格優(yōu)惠，歡迎垂詢訂購！我公司長期供應**組化抗體、WB抗體、**組化試劑盒和抗體試驗所需全部相關試劑、熒光標記抗體、單克隆抗體、多克隆抗體、各種標記的二抗IgG/IgM/IgD/IgA等科研實驗抗體。Anti-BPGM抗體用于**組化實驗,WB實驗,相應的標記抗體有HRP標記抗體,FITC標記,BIO等。
詳情介紹：
Rabbit Anti-BPGM
Cat. Number:
Anti-BPGM抗體KL-9519R
Quantity size:
0.2ml
Concentration:
1mg/ml Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
BPGM (2,3-bisphosphoglycerate mutase) Anti-BPGM抗體is a 259 amino acid protein that belongs to the phosphoglycerate mutase family and exists as a homodimer that plays a crucial role in the regulation of hemoglobin oxygen. Specifically, BPGM catalyzes the conversion of 3-phospho-D-glyceroyl phosphate to 2,3-bisphospho-D-glycerate (2,3-BPG), a reaction that is essential for controlling the concentration of 2,3-BPG within the cell. The gene encoding BPGM maps to human chromosome 7, which houses over 1,000 genes and comprises nearly 5% of the human genome. Defects in some of the genes Anti-BPGM抗體localized to chromosome 7 have been linked to Osteogenesis imperfecta, Williams-Beuren syndrome, Pendred syndrome, Lissencephaly, Citrullinemia and Shwachman-Diamond syndrome.
Involvement in disease:
Defects in BPGM are the cause of bisphosphoglycerate mutase deficiency (BPGMD) . A disease characterized by hemolytic anemia, splenomegaly, cholelithiasis and cholecystitis.
Involvement in disease:
Defects in BPGM are the cause of bisphosphoglycerate mutase deficiency (BPGMD) . A disease characterized by hemolytic anemia, splenomegaly, cholelithiasis and cholecystitis.
Also known as:
2,3-bisphosphoglycerate Anti-BPGM抗體mutase; 2,3-bisphosphoglycerate synthase; 3-bisphosphoglycerate mutase; 3-bisphosphoglycerate synthase; 3-diphosphoglycerate mutase; Ab2 098; AI323730; AL022789; Bisphosphoglycerate mutase; BPG dependent PGAM; BPG-dependent PGAM ; Bpgm; BPGM; C86192; DPGM; Erythrocyte 2,3 bisphosphoglycerate mutase; PMGE_HUMAN; 2,3-bisphosphoglycerate mutase, erythrocyte; erythrocyte; 2 antibody.
Specificity:
●
Rabbit Polyclonal IgG, affinity purified by Protein A.
●
Reacts with: Human, Mouse, Rat, Cow, Rabbit, Sheep, .
●
Immunogen: KLH conjugated synthetic peptide derived from human BPGM.
●
Predicted Molecular Weight: 30kDa.
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500 ELISA=1:500-1000Anti-BPGM抗體 IHC-P=1:100-500 IHC-F=1:100-500 IF=1:50-200
Not yet tested in other applications.
Optimal working dilutions must be determined by the end user.
Not yet tested in other applications.
Optimal working dilutions must be determined by the end user.
kl063Po01 白介素17(IL17)多克隆抗體 Polyclonal Antibody to Interleukin 17 (IL17)
kl063Ra01 白介素17(IL17)多克隆抗體 Polyclonal Antibody to Interleukin 17 (IL17)
kl064Bo01 白介素18(IL18)多克隆抗體 Polyclonal Antibody to Interleukin 18 (IL18)
kl064Ca01 白介素18(IL18)多克隆抗體 Polyclonal Antibody to Interleukin 18 (IL18)
kl064Cp01 白介素18(IL18)多克隆抗體 Polyclonal Antibody to Interleukin 18 (IL18)
kl064Eq01 白介素18(IL18)多克隆抗體 Polyclonal Antibody to Interleukin 18 (IL18)
kl064Ga01 白介素18(IL18)多克隆抗體 Polyclonal Antibody to Interleukin 18 (IL18)
kl064Po01 白介素18(IL18)多克隆抗體 Polyclonal Antibody to Interleukin 18 (IL18)
kl064Rb51 白介素18(IL18)多克隆抗體 Polyclonal Antibody to Interleukin 18 (IL18)
kl065Hu01 白介素1受體Ⅱ(IL1R2)多克隆抗體 Polyclonal Antibody to Interleukin 1 Receptor Type II (IL1R2)
kl065Mu01 白介素1受體Ⅱ(IL1R2)多克隆抗體 Polyclonal Antibody to Interleukin 1 Receptor Type II (IL1R2)
kl065Ra01 白介素1受體Ⅱ(IL1R2)多克隆抗體 Polyclonal Antibody to Interleukin 1 Receptor Type II (IL1R2)
kl065Si01 白介素1受體Ⅱ(IL1R2)多克隆抗體 Polyclonal Antibody to Interleukin 1 Receptor Type II (IL1R2)
kl066Hu01 白介素1受體Ⅰ(IL1R1)多克隆抗體 Polyclonal Antibody to Interleukin 1 Receptor Type I (IL1R1)
kl066Mu01 白介素1受體Ⅰ(IL1R1)多克隆抗體 Polyclonal Antibody to Interleukin 1 Receptor Type I (IL1R1)
kl066Ra01 白介素1受體Ⅰ(IL1R1)多克隆抗體 Polyclonal Antibody to Interleukin 1 Receptor Type I (IL1R1)
kl068Bo01 神經(jīng)膠質纖維酸性蛋白(GFAP)多克隆抗體 Polyclonal Antibody to Glial Fibrillary Acidic Protein (GFAP)
kl068Hu01 神經(jīng)膠質纖維酸性蛋白(GFAP)多克隆抗體 Polyclonal Antibody to Glial Fibrillary Acidic Protein (GFAP)
kl068Mu01 神經(jīng)膠質纖維酸性蛋白(GFAP)多克隆抗體 Polyclonal Antibody to Glial Fibrillary Acidic Protein (GFAP)
kl068Ra01 神經(jīng)膠質纖維酸性蛋白(GFAP)多克隆抗體 Polyclonal Antibody to Glial Fibrillary Acidic Protein (GFAP)
